High Frequency Chest Wall Oscillation in a Non-invasive Ventilation Dependent Patient With Spinal Muscular Atrophy Type 1.

With increased use of non-invasive positive pressure ventilation (NIPPV), the prognosis of children with neuromuscular disease (NMD) has improved significantly. However, children with muscle weakness remain at risk for recurrent respiratory infection or atelectasis. We report the case of a young girl with type 1 spinal muscular atrophy (SMA type 1), dependent on NIPPV, whose conventional physiotherapy management became insufficient to clear secretions and the use of high frequency chest wall oscillation (HFCWO) as a rescue therapy. This is the only case report that has shown HFCWO to assist in secretion clearance in a child severely weak with SMA type 1. Improvements were made in self ventilation time following the initiation of HFCWO. We advocate that when faced with severe respiratory infection and compromise in patients with NMD, HFCWO may be used safely in combination with conventional physiotherapy techniques.

Source : http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?tmpl=NoSidebarfile&db=PubMed&cmd=Retrieve&list_uids=21605484&dopt=Abstract

Partager